Difficult to treat desmoplastic reaction usually in mesentery.
- Associated with FAP
- Severity of desmoid reaction is inversely proportional to the number of polyps.
- therefore, some argue that pts with attenuated FAP with fewer polyps should have surgery delayed as long as possible to prolong the risk of developing post-op desmoid tumors
Treatment:
- treatment of desmoid tumors is limited.
- NO Surgery! Desmoplastic reaction only gets worse with each surgery
- only effective therapy is adriamycin based chemotherapy
No comments:
Post a Comment